CONGENITAL MIDLINE CERVICAL CLEFT: STUDY OF TWO CASES
Authors:
Anna Christou1, Zoe Nicolaou2, Eleftherios Kalimeras3
Affiliation:
1 Klinikum Stuttgart, Stuttgart, Germany
2 Director, Cyprus Cranio Maxillo Facial Center, Limassol, Cyprus
3 Head of Oral & Maxillofacial Surgery Department - Interbalkan Medical Center of Thessaloniki, Thessaloniki, Greece
Doi: 10.54936/haoms242p55
ABSTRACT:
Background: Midline cervical cleft (MCC) is a rare congenital developmental defect of the anterior neck of unclear etiology; however, an impaired fusion of the distal branchial arches in the midline is the most commonly accepted theory. It is usually presented in the neonatal period as usually as scarlike skin defect or cord-like contractive abnormality of the skin at the ventral neck and it is often linked to developmental defects such as cysts, bifid mandible and micrognathia as well as possible loss of the structures of hyoid bone. (MCC is an uncommon malformation of the anterior neck with unknown embryologic development. Until 2014 only 205 cases were reported).
Case presentation: Two cases of a congenital midline cervical cleft of a 2-year-old and of a 5-year-old Caucasian boy were presented in our craniofacial clinic. In the first case the anatomical limits of the lesion were from height of the isthmus of the thyroid to the base of tongue whereas in the second case the lesion was outlined as a cystic focus anterior to the upper aspect of the manubrium of the sternum without a sinus tract. There was no family history of clefts in both cases as well as normal vaginal delivery.
Discussion: In this report we will present the surgical treatment plan, focusing on preoperative and postoperative sequence. The surgical excision was performed with a double-Z plasty in order to achieve aesthetic and functional outcome.
Conclusion: Midline cervical cleft can be diagnosed by a pediatrician, an oral and maxillofacial surgeon, an orthodontist, an ENT or a plastic surgeon.
It is critical to get a diagnosis and treatment as soon as possible to reduce the likelihood of additional mandibular defects.
KEY WORDS:
Authors:
Anna Christou1, Zoe Nicolaou2, Eleftherios Kalimeras3
Affiliation:
1 Klinikum Stuttgart, Stuttgart, Germany
2 Director, Cyprus Cranio Maxillo Facial Center, Limassol, Cyprus
3 Head of Oral & Maxillofacial Surgery Department - Interbalkan Medical Center of Thessaloniki, Thessaloniki, Greece
Doi: 10.54936/haoms242p55
ABSTRACT:
Background: Midline cervical cleft (MCC) is a rare congenital developmental defect of the anterior neck of unclear etiology; however, an impaired fusion of the distal branchial arches in the midline is the most commonly accepted theory. It is usually presented in the neonatal period as usually as scarlike skin defect or cord-like contractive abnormality of the skin at the ventral neck and it is often linked to developmental defects such as cysts, bifid mandible and micrognathia as well as possible loss of the structures of hyoid bone. (MCC is an uncommon malformation of the anterior neck with unknown embryologic development. Until 2014 only 205 cases were reported).
Case presentation: Two cases of a congenital midline cervical cleft of a 2-year-old and of a 5-year-old Caucasian boy were presented in our craniofacial clinic. In the first case the anatomical limits of the lesion were from height of the isthmus of the thyroid to the base of tongue whereas in the second case the lesion was outlined as a cystic focus anterior to the upper aspect of the manubrium of the sternum without a sinus tract. There was no family history of clefts in both cases as well as normal vaginal delivery.
Discussion: In this report we will present the surgical treatment plan, focusing on preoperative and postoperative sequence. The surgical excision was performed with a double-Z plasty in order to achieve aesthetic and functional outcome.
Conclusion: Midline cervical cleft can be diagnosed by a pediatrician, an oral and maxillofacial surgeon, an orthodontist, an ENT or a plastic surgeon.
It is critical to get a diagnosis and treatment as soon as possible to reduce the likelihood of additional mandibular defects.
KEY WORDS: